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“The long journey of unexplained erythrocytosis”. Erythrocytosis due to high oxygen affinity hemoglobinopathy - hemoglobin variant Little Rock (HBB: c.432C>A) - A report of a Swiss Family and review of the literature
“The long journey of unexplained erythrocytosis”. Erythrocytosis due to high oxygen affinity hemoglobinopathy - hemoglobin variant Little Rock (HBB: c.432C>A) - A report of a Swiss Family and review of the literature
The differential diagnosis of erythrocytosis is complex, involving a tailored algorithm. Congenital causes are rare and su...
Waldenström macroglobulinemia and non-IgM-type lymphoplasmacytic lymphoma are genetically similar
Waldenström macroglobulinemia and non-IgM-type lymphoplasmacytic lymphoma are genetically similar
Introduction Waldenström macroglobulinemia (WM) represents a subset of lymphoplasmacytic lymphoma (LPL) with the imm...
The role of follicular regulatory T cells/follicular helper T cells in primary immune thrombocytopenia
The role of follicular regulatory T cells/follicular helper T cells in primary immune thrombocytopenia
Introduction Immune thrombocytopenia (ITP) is an autoimmune disease characterized by thrombocytopenia. Herein, we sought t...
Successful Multidisciplinary Management of Aortic Valve Repair in Severe Hemophilia B with Extended Half-Life Recombinant Factor IX concentrate
Successful Multidisciplinary Management of Aortic Valve Repair in Severe Hemophilia B with Extended Half-Life Recombinant Factor IX concentrate
Successful management of surgery in severe coagulation disorders depends on adequate replacement of the deficient factors ...
Description of an institutional cohort of myeloid neoplasms carrying ETV6-locus deletions or ETV6 rearrangements
Description of an institutional cohort of myeloid neoplasms carrying ETV6-locus deletions or ETV6 rearrangements
The gene encoding for transcription factor ETV6 presents recurrent lesions in hematologic neoplasms, most notably the ETV6...
Patient-reported Outcomes in Young Adults with Myeloproliferative Neoplasms
Patient-reported Outcomes in Young Adults with Myeloproliferative Neoplasms
Introduction Genetic landscape, disease characteristics and clinical outcomes of young adults with myeloproliferative neop...
Acquired von Willebrand syndrome following a SARS-CoV2 infection
Acquired von Willebrand syndrome following a SARS-CoV2 infection
Acquired von Willebrand syndrome is a rare entity with approximately 700 cases described in the literature. Many etiologie...
Macrocytosis in Mitochondrial DNA Deletion Syndromes
Macrocytosis in Mitochondrial DNA Deletion Syndromes
Large single mtDNA (mitochondrial DNA) deletion syndrome is a rare inborn error of metabolism with variable heteroplasmy l...
Therapeutic Efficacy of Platelet Transfusion And Analysis of Influencing Factors in 364 Patients
Therapeutic Efficacy of Platelet Transfusion And Analysis of Influencing Factors in 364 Patients
Introduction: In clinical diagnosis and treatment, we found that PLT counts failed to increase significantly or even decre...
Erdheim-Chester Disease with BRAF V600E Mutation and a Concomitant Myeloid Malignancy Sharing NRAS and IDH2 Mutations
Erdheim-Chester Disease with BRAF V600E Mutation and a Concomitant Myeloid Malignancy Sharing NRAS and IDH2 Mutations
Erdheim-Chester disease (ECD) is a rare clonal histiocytic process that is characterized by a foamy (xanthomatous) prolife...
High Expression of CD300A Predicts Poor Survival in Acute Myeloid Leukemia
High Expression of CD300A Predicts Poor Survival in Acute Myeloid Leukemia
Introduction: Recent studies have suggested that CD300A was an oncogene in acute myeloid leukemia (AML) development. Howev...
A Longitudinal Assessment of the Natural Change in Haemoglobin, Haematocrit and Mean Corpuscular Volume with Age
A Longitudinal Assessment of the Natural Change in Haemoglobin, Haematocrit and Mean Corpuscular Volume with Age
Introduction: We aim to assess the natural annual trends in the levels of haemoglobin, haematocrit and mean corpuscular vo...
Once Monthly Elotuzumab and Lenalidomide Plus Dexamethasone for Multiple Myeloma: A Multicenter Observation Study
Once Monthly Elotuzumab and Lenalidomide Plus Dexamethasone for Multiple Myeloma: A Multicenter Observation Study
<b><i>Introduction:</i></b> Elotuzumab and lenalidomide plus dexamethasone (ERd) is a standard sal...
Gene Variants in Two Families with Inherited Coagulation Factor XI Deficiency and Identification of Mutations
Gene Variants in Two Families with Inherited Coagulation Factor XI Deficiency and Identification of Mutations
<b><i>Introduction:</i></b> Mutations in the <i>F11</i> gene can cause factor XI (FXI)...
Disparity analysis of clinical features and prognostic evaluation of hemophagocytic lymphohistiocytosis in pediatric and adult patients: a retrospective multicenter study of 525 cases in HHLWG
Disparity analysis of clinical features and prognostic evaluation of hemophagocytic lymphohistiocytosis in pediatric and adult patients: a retrospective multicenter study of 525 cases in HHLWG
Introduction: Hemophagocytic lymphohistiocytosis (HLH) is a rare immune disorder with rapid progression and high mortality...
On behalf of the SFGM-TC: prophylactic donor lymphocyte infusion in patients treated with allogeneic stem-cell transplantation for high-risk myelodysplastic syndrome and acute myeloid leukemia
On behalf of the SFGM-TC: prophylactic donor lymphocyte infusion in patients treated with allogeneic stem-cell transplantation for high-risk myelodysplastic syndrome and acute myeloid leukemia
Introduction: Allogeneic hematopoietic stem cell transplantation (allo-HSCT) remains the best curative option for high-ris...
Two novel heterozygous mutations (p.γPhe230Val and p.AαAsn839Thr) cause hereditary hypodysfibrinogenemia in two Chinese independent families
Two novel heterozygous mutations (p.γPhe230Val and p.AαAsn839Thr) cause hereditary hypodysfibrinogenemia in two Chinese independent families
The objective of this study was to explore the molecular defects in two Chinese families with hypodysfibrinogenemia. The c...
High Incidences of Acute and Chronic Graft-Versus-Host Disease after Hematopoietic Cell Transplants for Acute Myeloid Leukemia Using Thiotepa, Busulfan, and Fludarabine Pretransplant Conditioning
High Incidences of Acute and Chronic Graft-Versus-Host Disease after Hematopoietic Cell Transplants for Acute Myeloid Leukemia Using Thiotepa, Busulfan, and Fludarabine Pretransplant Conditioning
...
Efficacy and incidence of treatment related adverse events of thrombopoietin receptor agonists in adults with immune thrombocytopenia: a systematic review and network meta-analysis of randomized controlled study
Efficacy and incidence of treatment related adverse events of thrombopoietin receptor agonists in adults with immune thrombocytopenia: a systematic review and network meta-analysis of randomized controlled study
Introduction: To conduct a network meta-analysis to assess the efficacy and incidence of treatment related adverse events ...
Gene Variants in Two Families with Inherited Coagulation Factor Ⅺ Deficiency and Identification of Mutations
Gene Variants in Two Families with Inherited Coagulation Factor Ⅺ Deficiency and Identification of Mutations
Abstract Introduction: Mutations in the F11 gene can cause factor Ⅺ (FⅪ) deficiency, leading to abnormal coagulation activ...
The effectiveness of the intermediate and therapeutic doses of enoxaparin in COVID-19 patients: A comparative study of factor Xa inhibition
The effectiveness of the intermediate and therapeutic doses of enoxaparin in COVID-19 patients: A comparative study of factor Xa inhibition
Background: Management of anticoagulant therapy in COVID-19 patients is a critical role. Low Molecular Weight Heparin (LMW...
Once monthly elotuzumab, lenalidomide plus dexamethasone for multiple myeloma; a multicenter observation study
Once monthly elotuzumab, lenalidomide plus dexamethasone for multiple myeloma; a multicenter observation study
Introduction: Elotuzumab, lenalidomide plus dexamethasone (ERd) is a standard salvage chemotherapy for multiple myeloma, a...
Glomerulonephritis Secondary to Acute Promyelocytic Leukemia that Resolved after Induction Therapy.
Glomerulonephritis Secondary to Acute Promyelocytic Leukemia that Resolved after Induction Therapy.
The association of glomerulonephritis and malignant hematological disease is uncommon, but well known in chronic leukemias...
Antithrombin Activity is Associated with Persistent Thromboinflammation and Mortality in Patients with Severe COVID-19 Illness
Antithrombin Activity is Associated with Persistent Thromboinflammation and Mortality in Patients with Severe COVID-19 Illness
Background: Severe COVID-19 illness can lead to thrombotic complications, organ failure, and death. Antithrombin (AT) regu...
The Challenging Management of Acute Thrombotic Microangiopathy in Pregnancy
The Challenging Management of Acute Thrombotic Microangiopathy in Pregnancy
Thrombotic microangiopathy is characterized by microangiopathic hemolytic anemia, thrombocytopenia, and end-organ injury. ...
High incidences of acute and chronic graft-versus-host disease after haematopoietic cell transplants for acute myeloid leukaemia using thiotepa, busulfan and fludarabine pretransplant conditioning
High incidences of acute and chronic graft-versus-host disease after haematopoietic cell transplants for acute myeloid leukaemia using thiotepa, busulfan and fludarabine pretransplant conditioning
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A Co-Management Model For Myeloid Malignancies that Evolved During the COVID-19 Pandemic
A Co-Management Model For Myeloid Malignancies that Evolved During the COVID-19 Pandemic
Introduction: Myeloid malignancies are a heterogenous group of clonal bone marrow disorders that are complex to manage in ...
Low rate of infectious enterocolitis in allogeneic stem cell transplant recipients with acute diarrhea: A prospective study by the GETH-TC.
Low rate of infectious enterocolitis in allogeneic stem cell transplant recipients with acute diarrhea: A prospective study by the GETH-TC.
Acute diarrhea is a common and debilitating complication in recipients of an allogeneic hematopoietic stem cell transplant...
Contents Vol. 145, 2022
Contents Vol. 145, 2022
Acta Haemato...
Resolution of Melanoma to Programmed Death-1 Blockade but Simultaneous Rapid Progression of Concomitant Chronic Lymphocytic Leukemia
Resolution of Melanoma to Programmed Death-1 Blockade but Simultaneous Rapid Progression of Concomitant Chronic Lymphocytic Leukemia
Here, we present a novel case of a patient with chronic lymphocytic leukemia (CLL) who received CTLA-4 and then PD-1 immun...
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