A flavoprotein enzyme that is responsible for the catabolism of LYSINE; HYDROXYLYSINE; and TRYPTOPHAN. It catalyzes the oxidation of GLUTARYL-CoA to crotonoyl-CoA using FAD as a cofactor. Glutaric aciduria type I is an inborn error of metabolism due to the deficiency of glutaryl-CoA dehydrogenase.
推出的年份: 2006(1973)
副标题
树号: D08.811.682.660.425
MeSH 单一 ID: D050770
进入的组:
Dehydrogenase, Glutaryl-CoA
Glutaryl-Coenzyme A Dehydrogenase
Dehydrogenase, Glutaryl-Coenzyme A
Glutaryl Coenzyme A Dehydrogenase
Glutaryl CoA Dehydrogenase
CoA Dehydrogenase, Glutaryl
Dehydrogenase, Glutaryl CoA
早前的内容:
Acyl Coenzyme A (1973-1979)
Coenzymes (1973-1979)
Glutarates (1973-1980)
Oxidoreductases (1983-2003)
Oxidoreductases Acting on CH-CH Group Donors (2004-2005)
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