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alpha 1-Antitrypsin Deficiency
Deficiency of the protease inhibitor ALPHA 1-ANTITRYPSIN that manifests primarily as PULMONARY EMPHYSEMA and LIVER CIRRHOSIS.
推出的年份: 1998
副标题
blood
cerebrospinal fluid
chemically induced
classification
complications
diagnosis
diagnostic imaging
diet therapy
drug therapy
economics
embryology
enzymology
epidemiology
ethnology
etiology
genetics
history
immunology
metabolism
microbiology
mortality
nursing
parasitology
pathology
physiopathology
prevention and control
psychology
radiotherapy
rehabilitation
surgery
therapy
urine
veterinary
virology
树号:
C06.552.074, C08.381.112, C16.320.060, C23.550.325.500.500
MeSH 单一 ID:
D019896
进入的组:
Deficiencies, alpha 1-Antitrypsin
Deficiency, alpha 1-Antitrypsin
alpha 1 Antitrypsin Deficiency
alpha 1-Antitrypsin Deficiencies
早前的内容:
alpha 1-Antitrypsin (1974)
alpha 1-Antitrypsin/deficiency (1975-1997)
All MeSH Categories
Diseases Category
Digestive System Diseases [C06]
Liver Diseases [C06.552]
alpha 1-Antitrypsin Deficiency [C06.552.074]
Budd-Chiari Syndrome [C06.552.347]
Chemical and Drug Induced Liver Injury [C06.552.100]
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Cholestasis, Intrahepatic [C06.552.150]
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Fatty Liver [C06.552.241]
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Focal Nodular Hyperplasia [C06.552.270]
Hepatic Infarction [C06.552.289]
Hepatic Insufficiency [C06.552.308]
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Hepatic Veno-Occlusive Disease [C06.552.360]
Hepatitis [C06.552.380]
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Hepatolenticular Degeneration [C06.552.413]
Hepatomegaly [C06.552.416]
Hepatopulmonary Syndrome [C06.552.455]
Hepatorenal Syndrome [C06.552.465]
Hypertension, Portal [C06.552.494]
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Liver Abscess [C06.552.597]
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Liver Cirrhosis [C06.552.630]
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Liver Diseases, Alcoholic [C06.552.645]
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Liver Diseases, Parasitic [C06.552.664]
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Liver Neoplasms [C06.552.697]
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Peliosis Hepatis [C06.552.802]
Porphyrias, Hepatic [C06.552.830]
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Tuberculosis, Hepatic [C06.552.933]
Zellweger Syndrome [C06.552.970]
All MeSH Categories
Diseases Category
Respiratory Tract Diseases [C08]
Lung Diseases [C08.381]
Acute Chest Syndrome [C08.381.074]
alpha 1-Antitrypsin Deficiency [C08.381.112]
Cystic Adenomatoid Malformation of Lung, Congenital [C08.381.150]
Cystic Fibrosis [C08.381.187]
Hemoptysis [C08.381.348]
Hepatopulmonary Syndrome [C08.381.385]
Hypertension, Pulmonary [C08.381.423]
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Lung Abscess [C08.381.450]
Lung Diseases, Fungal [C08.381.472]
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Lung Diseases, Interstitial [C08.381.483]
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Lung Diseases, Obstructive [C08.381.495]
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Lung Diseases, Parasitic [C08.381.517]
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Lung Injury [C08.381.520]
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Lung Neoplasms [C08.381.540]
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Lung, Hyperlucent [C08.381.570]
Plasma Cell Granuloma, Pulmonary [C08.381.600]
Pneumonia [C08.381.677]
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Pulmonary Alveolar Proteinosis [C08.381.719]
Pulmonary Atelectasis [C08.381.730]
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Pulmonary Edema [C08.381.742]
Pulmonary Embolism [C08.381.746]
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Pulmonary Eosinophilia [C08.381.750]
Pulmonary Veno-Occlusive Disease [C08.381.780]
Respiratory Distress Syndrome [C08.381.840]
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Scimitar Syndrome [C08.381.844]
Solitary Pulmonary Nodule [C08.381.884]
Tuberculosis, Pulmonary [C08.381.922]
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All MeSH Categories
Diseases Category
Congenital, Hereditary, and Neonatal Diseases and Abnormalities [C16]
Genetic Diseases, Inborn [C16.320]
Adrenal Hyperplasia, Congenital [C16.320.033]
Alagille Syndrome [C16.320.051]
alpha 1-Antitrypsin Deficiency [C16.320.060]
Anemia, Hemolytic, Congenital [C16.320.070]
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Anemia, Hypoplastic, Congenital [C16.320.077]
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Ataxia Telangiectasia [C16.320.080]
Autoimmune Lymphoproliferative Syndrome [C16.320.089]
Blood Coagulation Disorders, Inherited [C16.320.099]
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Brugada Syndrome [C16.320.100]
CADASIL [C16.320.129]
Camurati-Engelmann Syndrome [C16.320.144]
Cardiomyopathy, Hypertrophic, Familial [C16.320.160]
CHARGE Syndrome [C16.320.165]
Cherubism [C16.320.170]
Chromosome Disorders [C16.320.180]
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Ciliopathies [C16.320.184]
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Costello Syndrome [C16.320.188]
Cystic Fibrosis [C16.320.190]
Donohue Syndrome [C16.320.215]
Dwarfism [C16.320.240]
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Eye Diseases, Hereditary [C16.320.290]
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Familial Multiple Lipomatosis [C16.320.298]
Frasier Syndrome [C16.320.306]
GATA2 Deficiency [C16.320.314]
Genetic Diseases, X-Linked [C16.320.322]
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Genetic Diseases, Y-Linked [C16.320.338]
Hajdu-Cheney Syndrome [C16.320.355]
Hemoglobinopathies [C16.320.365]
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Hereditary Autoinflammatory Diseases [C16.320.382]
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Heredodegenerative Disorders, Nervous System [C16.320.400]
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Hyper-IgM Immunodeficiency Syndrome [C16.320.413]
Hyperthyroxinemia, Familial Dysalbuminemic [C16.320.427]
Kallmann Syndrome [C16.320.467]
Kartagener Syndrome [C16.320.184.500.531]
Laminopathies [C16.320.488]
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Lennox Gastaut Syndrome [C16.320.495]
Loeys-Dietz Syndrome [C16.320.510]
Marfan Syndrome [C16.320.540]
Metabolism, Inborn Errors [C16.320.565]
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Muscular Dystrophies [C16.320.577]
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Myasthenic Syndromes, Congenital [C16.320.590]
Nail-Patella Syndrome [C16.320.600]
Neoplastic Syndromes, Hereditary [C16.320.700]
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Oculocerebrorenal Syndrome [C16.320.322.750]
Orofaciodigital Syndromes [C16.320.180.830.670]
Osteoarthropathy, Primary Hypertrophic [C16.320.718]
Osteochondrodysplasias [C16.320.728]
Osteogenesis Imperfecta [C16.320.737]
Pain Insensitivity, Congenital [C16.320.775]
Pelger-Huet Anomaly [C16.320.784]
Primary Immunodeficiency Diseases [C16.320.798]
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Pycnodysostosis [C16.320.565.595.800]
Renal Tubular Transport, Inborn Errors [C16.320.565.893]
Skin Diseases, Genetic [C16.320.850]
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Werner Syndrome [C16.320.925]
Yellow Nail Syndrome [C16.320.962]
All MeSH Categories
Diseases Category
Pathological Conditions, Signs and Symptoms [C23]
Pathologic Processes [C23.550]
Emphysema [C23.550.325]
Subcutaneous Emphysema [C23.550.325.500]
alpha 1-Antitrypsin Deficiency [C23.550.325.500.500]
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