Salivary duct cyst (SDC) is a true salivary gland pathology that rarely occurs in the upper lip. The proposed rarity of SDC is around 0.39% of all the salivary cystic lesions. It usually arises in the lower lip or the floor of the mouth and is prevalent in the sixth/eight decade of life. We report a case of 76-year-old male patient with a chief complaint of an abnormal growth of the upper lip. The growth had increased in size from the last two months. Clinically it was a well circumscribed, solitary, nodular, painless, mobile, noncompressible, soft growth. Excisional biopsy was performed. Histology revealed a SDC and sialolithiasis in the upper lip. This article aims to include SDC in the differential diagnosis of lesions in the upper lip. Their clinical and histopathology features mimic salivary gland pathology such as mucocele, pleomorphic adenoma, basal cell adenoma, low-grade mucoepidermoid carcinoma.