This is a retrospective, descriptive study of 08 children with ACAPA followed in the unit of cardio-paediatrics of the cardiac department, Ibn ROCHD Hospital, over a period of 5 years from September 2018 to September 2023.

The prevalence of ACAPA compared to the number of congenital heart diseases diagnosed during the same study period: 0.16%.

Distribution:

– 2 ALCAPA, and 6 ARCAPA;

– 5 boys, 3 girls;

– Average age: 1 year 9 months.

The most frequent reason for consultation is a food difficulty with the signs respiratory.

ECG showed in 2 patients a Q wave of necrosis which is a very specific sign of the disease.

TTE: shows indirect signs such as hypokinetic dilated cardiomyopathy which is present in all our patients, valvular leaks are also frequent. Direct signs are less frequent and difficult to objectivise: absence of visualization of the origin of the coronary artery a the base of the aorta, or visualization of the hyper refractile endocardium, with image abnormal birth of a coronary artery.

Cardiac catheterization with angiography is performed in case of diagnostic doubt.

After the positive diagnosis, 5 of our patients underwent surgery, only 1 patient died in the post-operative follow-up, the evolution was favorable for the 4 other patients.