Background Omphalocele is a congenital abnormality of the abdominal wall consisting of protrusion of the abdominal contents at the base of the umbilical cord. It is associated with genetic and structural defects, which significantly affect its prognosis and survival outcomes.

Case Presentation Prenatal diagnosis of this condition is crucial for apt management; however, we present two cases of neglected and giant omphaloceles in early childhood. It is usually a disease of neonatal age, and presentation at such a late age is quite rare. The management of such cases is quite challenging, and multiple strategies have been described. In our case, the giant omphalocele was managed with an external surgical skin closure system as a component of a staged closure strategy.

Conclusion The expert surgical technique played a decisive role, allowing the coordination of a multidisciplinary team, which was crucial for optimal management.

A written informed consent was obtained from the participants.

The cases and the images are available from the Department of Radiodiagnosis, Vardhman Mahavir Medical College and Safdarjung Hospital, New Delhi, India.

N.B. is the corresponding author, designed and revised the work, interpreted the data, submitted the case, drafted the work, and approved the submitted version for publication. R.M. contributed to revision of the manuscript and approved the submitted version for publication. R.M. and P.M. contributed to revision of the work. J.G. provided the subjects for the study. All authors read and approved the final manuscript.

Article published online:
03 October 2024

© 2024. The Author(s). This is an open access article published by Thieme under the terms of the Creative Commons Attribution License, permitting unrestricted use, distribution, and reproduction so long as the original work is properly cited. (https://creativecommons.org/licenses/by/4.0/)

Thieme Medical and Scientific Publishers Pvt. Ltd.
A-12, 2nd Floor, Sector 2, Noida-201301 UP, India