Hydatidosis is a cosmopolitan zoonosis caused by a cestode known as Echinococcus granuloses [1]. It leads to the development of one or several unilocular fluid-filled hydatid cysts, that mainly form in the liver (75%) and in the lungs (15.4%), but that can also occur in any part of the body [2]. The life cycle of E. granulosus depends on two host species to complete. The definitive hosts are typically dogs and wolves, which get infected by ingesting hydatid cysts containing viable protoscolices. In the canine’s intestinal tract, protoscolices evaginate, attach to the intestinal mucosa and develop into adult stages. The adult worms then release their eggs in the environment through feces. Following the ingestion of eggs by an intermediate host such as humans, sheep, goats, pigs, cattle, horses, and camels, an oncosphere larva is released in the intestinal tract, penetrate the intestinal mucosa and travel through the blood or lymphatic circulation to different organs, mainly the liver and the lungs. The larva then becomes a metacestode and develops into a hydatid cyst [3], [4]. Eventually, protoscolices form in the metacestode, and will allow for the infection of another definitive host if the hydatid cyst is ingested [3]. Rare are the regions of the world which are completely free of E. granulosus, but transmission rates differ drastically from region to region. The global distribution seems to be linked to the extensiveness of animal husbandry and livestock production, and to the presence of dogs (e.g. dogs used for guarding livestock, or dogs that have access to carcasses and offal of dead livestock) [3]. The greatest prevalence of cystic echinococcosis (CE) in humans and animal hosts can be found in the Mediterranean regions, southern and central parts of Russia, central Asia, China, Australia, some parts of America (especially South America) and north and east Africa [3]. CE prevalence varies greatly globally; for instance, it reaches 4–8/100,000 in the most affected regions of Europe (southern Italy, Sardinia and pars of Spain) and 2% in sheep-raising areas of Tunisia and Libya [4]. Splenic hydatid cyst (SHC) is an extremely rare disease, even in endemic areas, its frequency ranging from 0.5 to 4% of all cases of echinococcosis [8]. SHC can either be primary (located exclusively in the spleen) or secondary (accompanied by hydatid cysts in other organs) [6]. Complications include fistulisation into nearby organs like the stomach or the pancreas, secondary hypertension due to left renal artery compression, or even anaphylactic shock due to spontaneous or traumatic cyst rupture or during surgery. Total splenectomy is the treatment advocated by the majority of surgeons [5], [6], [7].