Gupta N, Finlay GA, Kotloff RM, Strange C, Wilson KC, Young LR, et al. Lymphangioleiomyomatosis diagnosis and management: high-resolution chest computed tomography, transbronchial lung biopsy, and pleural disease management. An Official American Thoracic Society/Japanese Respiratory Society Clinical Practice Guideline. Am J Respir Crit Care Med. 2017;196:1337–48.

Article  Google Scholar 

Hayashida M, Seyama K, Inoue Y, Fujimoto K, Kubo K, Respiratory Failure Research Group of the Japanese Ministry of Health L, et al. The epidemiology of lymphangioleiomyomatosis in Japan: a nationwide cross-sectional study of presenting features and prognostic factors. Respirology. 2007;12:523–30.

Article  Google Scholar 

Harknett EC, Chang WY, Byrnes S, Johnson J, Lazor R, Cohen MM, et al. Use of variability in national and regional data to estimate the prevalence of lymphangioleiomyomatosis. QJM. 2011;104:971–9.

CAS  Article  Google Scholar 

McCormack FX. Lymphangioleiomyomatosis: a clinical update. Chest. 2008;133:507–16.

CAS  Article  Google Scholar 

Gupta N, Lee HS, Ryu JH, Taveira-DaSilva AM, Beck GJ, Lee JC, et al. The NHLBI LAM registry: prognostic physiologic and radiologic biomarkers emerge from a 15-year prospective longitudinal analysis. Chest. 2019;155:288–96.

Article  Google Scholar 

Johnson SR, Cordier JF, Lazor R, Cottin V, Costabel U, Harari S, et al. European Respiratory Society guidelines for the diagnosis and management of lymphangioleiomyomatosis. Eur Respir J. 2010;35:14–26.

CAS  Article  Google Scholar 

Almoosa KF, Ryu JH, Mendez J, Huggins JT, Young LR, Sullivan EJ, et al. Management of pneumothorax in lymphangioleiomyomatosis: effects on recurrence and lung transplantation complications. Chest. 2006;129:1274–81.

Article  Google Scholar 

Kurihara M, Mizobuchi T, Kataoka H, Sato T, Kumasaka T, Ebana H, et al. A total pleural covering for lymphangioleiomyomatosis prevents pneumothorax recurrence. PLoS ONE. 2016;11: e0163637.

Article  Google Scholar 

McCormack FX, Inoue Y, Moss J, Singer LG, Strange C, Nakata K, et al. Efficacy and safety of sirolimus in lymphangioleiomyomatosis. N Engl J Med. 2011;364:1595–606.

CAS  Article  Google Scholar 

Ando K, Kurihara M, Kataoka H, Ueyama M, Togo S, Sato T, et al. Efficacy and safety of low-dose sirolimus for treatment of lymphangioleiomyomatosis. Respir Investig. 2013;51:175–83.

Article  Google Scholar 

Suina K, Hayashi T, Mitani K, Suzuki K, Takahashi K, Seyama K. What׳s the role of sirolimus on the treatment of lymphangioleiomyomatosis (LAM)?: Merely tuning up of LAM-associated dysfunctional lymphatic vessels rather than cytoreduction? Respir Investig. 2014;52(4):274–6.

Article  Google Scholar 

Oishi H, Watanabe T, Matsuda Y, Noda M, Ejima Y, Saiki Y, et al. Single lung transplantation for lymphangioleiomyomatosis: a single-center experience in Japan. Surg Today. 2018;48:944–50.

CAS  Article  Google Scholar 

Nakagiri T, Shintani Y, Minami M, Inoue M, Funaki S, Kawamura T, et al. Lung transplantation for lymphangioleiomyomatosis in a single japanese institute, with a focus on late-onset complications. Transplant Proc. 2015;47:1977–82.

CAS  Article  Google Scholar 

Suzuki K, Saji H, Aokage K, Watanabe SI, Okada M, Mizusawa J, et al. Comparison of pulmonary segmentectomy and lobectomy: safety results of a randomized trial. J Thorac Cardiovasc Surg. 2019;158:895–907.

Article  Google Scholar 

Reynaud-Gaubert M, Mornex JF, Mal H, Treilhaud M, Dromer C, Quétant S, et al. Lung transplantation for lymphangioleiomyomatosis: the French experience. Transplantation. 2008;86:515–20.

Article  Google Scholar 

Machuca TN, Losso MJ, Camargo SM, Schio SM, Melo IA, Hochhegger B, et al. Lung transplantation for lymphangioleiomyomatosis: single-center Brazilian experience with no chylothorax. Transplant Proc. 2011;43:236–8.

CAS  Article  Google Scholar 

Johnson SR. Lymphangioleiomyomatosis. Eur Respir J. 2006;27:1056–65.

CAS  Article  Google Scholar 

Ryu JH, Moss J, Beck GJ, Lee JC, Brown KK, Chapman JT, et al. The NHLBI lymphangioleiomyomatosis registry: characteristics of 230 patients at enrollment. Am J Respir Crit Care Med. 2006;173:105–11.

Article  Google Scholar 

Lama A, Ferreiro L, Golpe A, Gude F, Álvarez-Dobaño JM, González-Barcala FJ, et al. Characteristics of patients with lymphangioleiomyomatosis and pleural effusion: a systematic review. Respiration. 2016;91:256–64.

Article  Google Scholar 

Ryu JH, Doerr CH, Fisher SD, Olson EJ, Sahn SA. Chylothorax in lymphangioleiomyomatosis. Chest. 2003;123:623–7.

Article  Google Scholar 

Calvo E, Amarillas L, Mateos MA, Orradre JL, Gilsanz G, Alvarez-Sala JL, et al. Lymphangioleiomyomatosis, chylous ascites, and diet. Dig Dis Sci. 1996;41:591–3.

CAS  Article  Google Scholar 

Ko Y, Asakawa K, Tobino K, Oguma T, Hirai T, Takada T, et al. Quantitative analysis of computed tomography of the lungs in patients with lymphangioleiomyomatosis treated with sirolimus. Heliyon. 2020;6: e03345.

Article  Google Scholar 

Ando K, Okada Y, Akiba M, Kondo T, Kawamura T, Okumura M, et al. Lung transplantation for lymphangioleiomyomatosis in Japan. PLoS ONE. 2016;11: e0146749.

Article  Google Scholar 

Groetzner J, Kur F, Spelsberg F, Behr J, Frey L, Bittmann I, et al. Airway anastomosis complications in de novo lung transplantation with sirolimus-based immunosuppression. J Heart Lung Transplant. 2004;23:632–8.

Article  Google Scholar 

King-Biggs MB, Dunitz JM, Park SJ, Kay Savik S, Hertz MI. Airway anastomotic dehiscence associated with use of sirolimus immediately after lung transplantation. Transplantation. 2003;75:1437–43.

Article  Google Scholar